Pleuroparenchymal fibroelastosis (PPFE) is characterized by predominantly upper lobe pleural and subjacent parenchymal fibrosis; PPFE features were described in patients with rheumatic autoimmune diseases (RAID). A systematic literature review was performed to investigate the prevalence, prognosis and potential association of PPFE with previous immunosuppression in RAID.
Orlandi, M., Landini, N., Bruni, C., Sambataro, G., Nardi, C., Bargagli, E., et al. (2020). Pleuroparenchymal fibroelastosis in rheumatic autoimmune diseases: a systematic literature review. RHEUMATOLOGY, 59(12), 3645-3656 [10.1093/rheumatology/keaa451].
Pleuroparenchymal fibroelastosis in rheumatic autoimmune diseases: a systematic literature review
Bargagli, Elena;
2020-01-01
Abstract
Pleuroparenchymal fibroelastosis (PPFE) is characterized by predominantly upper lobe pleural and subjacent parenchymal fibrosis; PPFE features were described in patients with rheumatic autoimmune diseases (RAID). A systematic literature review was performed to investigate the prevalence, prognosis and potential association of PPFE with previous immunosuppression in RAID.File in questo prodotto:
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