Background Ewing Sarcoma (ES) and Neuroblastoma (NB) belong to a family of tumours of primitive neuroectodermal origin (PNET) that occurs in both bone and soft tissue. Notwithstanding ES and NB are two distinct malignant tumours, sometimes there could be a link between them. Case report We describe a case of an extraosseous ES localized in the retrosternal region and the upper lobe of the right lung, which had been previously treated for NB in a 6 years old female. We treated this case with a clamshell approach which allows, in a one-step surgery, a complete excision of the mass reconstructing the hemysternectomy with a non-crosslinked matrix. Conclusion the clamshell approach is therefore useful to achieve the retrosternal space and the lung with a single surgical access. According to our experience, we consider appropriate to use a non-crosslinked matrix for sternal reconstruction.

Molinaro, F., Angotti, R., Pellegrino, C., Casini, L., Luzzi, L., Paladini, P., et al. (2017). Surgical treatment of retrosternal extraosseous Ewing Sarcoma in a 6-years old female: A clamshell approach with hemysternectomy and application of a non-crosslinked extracellular matrix. JOURNAL OF PEDIATRIC SURGERY CASE REPORTS, 22, 9-13 [10.1016/j.epsc.2017.05.001].

Surgical treatment of retrosternal extraosseous Ewing Sarcoma in a 6-years old female: A clamshell approach with hemysternectomy and application of a non-crosslinked extracellular matrix

MOLINARO, FRANCESCO
;
Angotti, Rossella;Luzzi, Luca;PALADINI, PIERO;MESSINA, MARIO
2017-01-01

Abstract

Background Ewing Sarcoma (ES) and Neuroblastoma (NB) belong to a family of tumours of primitive neuroectodermal origin (PNET) that occurs in both bone and soft tissue. Notwithstanding ES and NB are two distinct malignant tumours, sometimes there could be a link between them. Case report We describe a case of an extraosseous ES localized in the retrosternal region and the upper lobe of the right lung, which had been previously treated for NB in a 6 years old female. We treated this case with a clamshell approach which allows, in a one-step surgery, a complete excision of the mass reconstructing the hemysternectomy with a non-crosslinked matrix. Conclusion the clamshell approach is therefore useful to achieve the retrosternal space and the lung with a single surgical access. According to our experience, we consider appropriate to use a non-crosslinked matrix for sternal reconstruction.
2017
Molinaro, F., Angotti, R., Pellegrino, C., Casini, L., Luzzi, L., Paladini, P., et al. (2017). Surgical treatment of retrosternal extraosseous Ewing Sarcoma in a 6-years old female: A clamshell approach with hemysternectomy and application of a non-crosslinked extracellular matrix. JOURNAL OF PEDIATRIC SURGERY CASE REPORTS, 22, 9-13 [10.1016/j.epsc.2017.05.001].
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Utilizza questo identificativo per citare o creare un link a questo documento: https://hdl.handle.net/11365/1011353